Mitochondrial Respiratory Chain

Sequential damage in mitochondrial complexes by peroxidative stress

Mitochondria / Biological Sciences / Electron Transfer / Animals / Male / Cytochrome C / Glutathione / Mitochondrial Respiratory Chain / Electron Transport / Cytochrome oxidase / Enzyme / Cytochrome B / Rats / Specific Activity / Side Effect / Pantothenic Acid / Succinate Dehydrogenase / Oxidation-Reduction / Citrate Synthase / Drug treatment / Gamma-Aminobutyric Acid / Neurochemical / Cytochrome C / Glutathione / Mitochondrial Respiratory Chain / Electron Transport / Cytochrome oxidase / Enzyme / Cytochrome B / Rats / Specific Activity / Side Effect / Pantothenic Acid / Succinate Dehydrogenase / Oxidation-Reduction / Citrate Synthase / Drug treatment / Gamma-Aminobutyric Acid / Neurochemical

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Low Brain Intracellular Free Magnesium in Mitochondrial Cytopathies

Neuroscience / Neurology / Metabolism / Magnetic Resonance Spectroscopy / Adolescent / Energy Metabolism / Phosphorus / Brain / Neurovascular / Humans / Magnesium / Flow / Brain Circulation / Female / Male / Mitochondrial Respiratory Chain / Cytoprotection / Free Energy / Enzyme / Clinical Sciences / Aged / Middle Aged / Cerebral / Adult / Neurosciences / Energy Metabolism / Phosphorus / Brain / Neurovascular / Humans / Magnesium / Flow / Brain Circulation / Female / Male / Mitochondrial Respiratory Chain / Cytoprotection / Free Energy / Enzyme / Clinical Sciences / Aged / Middle Aged / Cerebral / Adult / Neurosciences

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Respiratory chain deficiency presenting as congenital nephrotic syndrome

Membrane Proteins / Biopsy / Humans / Kidney / Female / Male / Mitochondrial Respiratory Chain / Differential Diagnosis / Pediatric Nephrology / Proteins / Pediatric / Newborn Infant / Mitochondrial Diseases / Renal disease / Nephrotic syndrome / Male / Mitochondrial Respiratory Chain / Differential Diagnosis / Pediatric Nephrology / Proteins / Pediatric / Newborn Infant / Mitochondrial Diseases / Renal disease / Nephrotic syndrome

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Influence of mitochondrial DNA level on cellular energy metabolism: implications for mitochondrial diseases

Bioenergetics / Energy Metabolism / Cell line / Mitochondrial DNA / Humans / Computer Simulation / Animals / Mitochondrial Respiratory Chain / Mitochondrial Diseases / Energy Production / Oxidative phosphorylation / Biochemistry and cell biology / Computer Simulation / Animals / Mitochondrial Respiratory Chain / Mitochondrial Diseases / Energy Production / Oxidative phosphorylation / Biochemistry and cell biology

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Mitochondrial disease in superoxide dismutase 2 mutant mice

Mitochondria / DNA damage / Multidisciplinary / Brain / Reactive Oxygen Species / Mice / Female / Animals / Male / Mitochondrial Respiratory Chain / Superoxide Dismutase / Enzyme / Oxidative phosphorylation / Carboxylic Acids / Oxidative Dna Damage / Succinate Dehydrogenase / Tissue Specificity / Mice / Female / Animals / Male / Mitochondrial Respiratory Chain / Superoxide Dismutase / Enzyme / Oxidative phosphorylation / Carboxylic Acids / Oxidative Dna Damage / Succinate Dehydrogenase / Tissue Specificity

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Complex V TMEM70 deficiency results in mitochondrial nucleoid disorganization

Genetics / Electron Microscopy / Membrane Proteins / Mitochondria / Tomography / Mitochondrial DNA / Humans / Mutation / Female / Male / ATP synthase / Mitochondrial Respiratory Chain / Newborn Infant / Mitochondrial Diseases / Adult / Cardiomyopathies / Human Fibroblasts / Mitochondrion / Mitochondrial DNA / Humans / Mutation / Female / Male / ATP synthase / Mitochondrial Respiratory Chain / Newborn Infant / Mitochondrial Diseases / Adult / Cardiomyopathies / Human Fibroblasts / Mitochondrion

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Mitochondrial disease in superoxide dismutase 2 mutant mice

Mitochondria / DNA damage / Multidisciplinary / Brain / Reactive Oxygen Species / Mice / Female / Animals / Male / Mitochondrial Respiratory Chain / Superoxide Dismutase / Enzyme / Oxidative phosphorylation / Carboxylic Acids / Oxidative Dna Damage / Succinate Dehydrogenase / Tissue Specificity / Mice / Female / Animals / Male / Mitochondrial Respiratory Chain / Superoxide Dismutase / Enzyme / Oxidative phosphorylation / Carboxylic Acids / Oxidative Dna Damage / Succinate Dehydrogenase / Tissue Specificity

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Complex V TMEM70 deficiency results in mitochondrial nucleoid disorganization

Genetics / Electron Microscopy / Membrane Proteins / Mitochondria / Tomography / Mitochondrial DNA / Humans / Mutation / Female / Male / ATP synthase / Mitochondrial Respiratory Chain / Newborn Infant / Mitochondrial Diseases / Adult / Cardiomyopathies / Human Fibroblasts / Mitochondrial DNA / Humans / Mutation / Female / Male / ATP synthase / Mitochondrial Respiratory Chain / Newborn Infant / Mitochondrial Diseases / Adult / Cardiomyopathies / Human Fibroblasts

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Complex V TMEM70 deficiency results in mitochondrial nucleoid disorganization

Genetics / Electron Microscopy / Membrane Proteins / Mitochondria / Tomography / Mitochondrial DNA / Humans / Mutation / Female / Male / ATP synthase / Mitochondrial Respiratory Chain / Newborn Infant / Mitochondrial Diseases / Adult / Cardiomyopathies / Human Fibroblasts / Mitochondrial DNA / Humans / Mutation / Female / Male / ATP synthase / Mitochondrial Respiratory Chain / Newborn Infant / Mitochondrial Diseases / Adult / Cardiomyopathies / Human Fibroblasts

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Gamma carbonic anhydrase like complex interact with plant mitochondrial complex I

Genetics / Plant Biology / Mitochondria / Plant Molecular Biology / Arabidopsis thaliana / Plant evolution / Phylogeny / Mitochondrial Respiratory Chain / Arabidopsis / Active site / Carbonic anhydrase / Isoenzymes / Genetic variation / Amino Acid Profile / Plant species / Plant Mitochondria / Yeasts / Two-Dimensional Gel Electrophoresis / Protein Binding / Two dimensional Gel Electrophoresis / Structural model / Biochemistry and cell biology / Dimerization / Plant evolution / Phylogeny / Mitochondrial Respiratory Chain / Arabidopsis / Active site / Carbonic anhydrase / Isoenzymes / Genetic variation / Amino Acid Profile / Plant species / Plant Mitochondria / Yeasts / Two-Dimensional Gel Electrophoresis / Protein Binding / Two dimensional Gel Electrophoresis / Structural model / Biochemistry and cell biology / Dimerization

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Two components in pathogenic mechanism of mitochondrial ATPase deficiency: Energy deprivation and ROS production

Mitochondria / Energy Metabolism / Humans / Reactive Oxygen Species / Mitochondrial Respiratory Chain / Enzyme / Experimental / Membrane Potential / Mitochondrial Membrane Potential / Adenosine Triphosphate / Production Rate / Enzyme / Experimental / Membrane Potential / Mitochondrial Membrane Potential / Adenosine Triphosphate / Production Rate

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Carvedilol improves energy production during acute global myocardial ischaemia

Energy Metabolism / Congestive Heart Failure / Animals / Mitochondrial Respiratory Chain / European / Energy Production / Rats / Wistar Rats / Energy Production / Rats / Wistar Rats

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AIF deficiency compromises oxidative phosphorylation

Membrane Proteins / Mitochondria / Apoptosis / Biological Sciences / Phylogeny / Brain / Humans / Glucose / Mice / Animals / Retina / Retinal Degeneration / Mitochondrial Respiratory Chain / Programmed cell death / Myocardium / Oxidative phosphorylation / Yeasts / Homologous Recombination / Lactic Acid / Adenosine Triphosphate / Brain / Humans / Glucose / Mice / Animals / Retina / Retinal Degeneration / Mitochondrial Respiratory Chain / Programmed cell death / Myocardium / Oxidative phosphorylation / Yeasts / Homologous Recombination / Lactic Acid / Adenosine Triphosphate

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Low Brain Intracellular Free Magnesium in Mitochondrial Cytopathies

Magnetic Resonance Spectroscopy / Adolescent / Energy Metabolism / Phosphorus / Brain / Humans / Magnesium / Female / Male / Mitochondrial Respiratory Chain / Cytoprotection / Free Energy / Enzyme / Clinical Sciences / Aged / Middle Aged / Cerebral / Adult / Neurosciences / Humans / Magnesium / Female / Male / Mitochondrial Respiratory Chain / Cytoprotection / Free Energy / Enzyme / Clinical Sciences / Aged / Middle Aged / Cerebral / Adult / Neurosciences

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Immunohistochemical detection of human mtDNA polymerase gamma and of human mitochondrial transcription factor A in cytochrome-c-oxidase-deficient oxyphil cells of hyperfunctional parathyroids

Transcription Factors / In Situ Hybridization / Mitochondrial DNA / Humans / Cytochrome c oxidase / Mitochondrial Respiratory Chain / Transcription Factor / Clinical Sciences / Hyperparathyroidism / DNA binding proteins / DNA Polymerase / Mitochondrial Respiratory Chain / Transcription Factor / Clinical Sciences / Hyperparathyroidism / DNA binding proteins / DNA Polymerase

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Giardia lamblia encodes a functional flavohemoglobin

Protein Structure and Function / Nitric oxide / Mitochondrial Respiratory Chain / Heme / NADPH oxidase / Single Cell / Amino Acid Sequence / Genetic Code / Small Intestine / Biochemistry and cell biology / Functional Properties / Single Cell / Amino Acid Sequence / Genetic Code / Small Intestine / Biochemistry and cell biology / Functional Properties

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